TY - JOUR T1 - Haemothorax in vascular Ehlers-Danlos syndrome JO - Reumatología Clínica (English Edition) T2 - AU - Álvarez,Kevin AU - López,Jordi AU - Hernández,Jose Angel SN - 21735743 M3 - 10.1016/j.reumae.2017.08.011 DO - 10.1016/j.reumae.2017.08.011 UR - https://www.reumatologiaclinica.org/en-haemothorax-in-vascular-ehlers-danlos-syndrome-articulo-S2173574319301121 AB - Vascular Ehlers-Danlos syndrome (EDS IV) is a rare genetic disorder characterised by an alteration in the COL3A1 gene which encodes type III collagen. It is the most common type of collagen in vessels of medium size and certain organs such as the intestines and the uterus. The alteration of this type of collagen produces aneurisms and ruptures of vessels and organs. A high level of clinical suspicion is required for diagnosis. It is a complex disease whose management requires a multidisciplinary team to treat the different complications that may occur.We report the case of a 50-year-old man diagnosed with EDS IV detected incidentally after haemothorax secondary to a coughing spell. ER -