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Vol. 7. Issue 1.
Pages 61-67 (January - February 2011)
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Vol. 7. Issue 1.
Pages 61-67 (January - February 2011)
Clinicopathologic conference
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Rapidly progressive fatal interstitial lung disease in a patient with an overlap syndrome of systemic lupus erythematosus and systemic sclerosis
Enfermedad pulmonar intersticial rápidamente progresiva y fatal en una paciente con síndrome de superposición de lupus eritematoso sistémico y esclerosis sistémica
Mónica P. Sacnuna, Jaime Ferrerb, Marisol Ferrerb, Bernardo A. Pons-Estelc,
Corresponding author
a Servicio de Reumatología y Colagenopatías, Hospital Provincial de Rosario, Rosario, Argentina
b Servicio de Anatomía Patológica, Sanatorio Parque, Rosario, Argentina
c Servicio de Reumatología, Instituto Cardiovascular de Rosario, Rosario, Argentina
Article information

A 31-year-old woman with a prior history of an overlap syndrome of systemic lupus erythematosus (SLE) and systemic sclerosis (SSc) developed fever, pericarditis with pericardial effusion and a rapidly progressive fatal interstitial lung disease. Diagnostic test and procedures, differential diagnosis and therapeutic approach are discussed.

Interstitial lung disease
Overlap syndrome

Paciente de 31 años, con historia de síndrome de superposición de lupus eritematoso sistémico y esclerosis sistémica que desarrolla un cuadro caracterizado por fiebre, pericarditis con derrame pericárdico y enfermedad pulmonar rápidamente progresiva y fatal. Se discuten aspectos diagnósticos e indicaciones terapéuticas.

Palabras clave:
Enfermedad intersticial pulmonar
Síndrome de superposición
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Reumatología Clínica (English Edition)

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