CongenitalMadelung’s Deformity: A Spectrum of Presentation
Section snippets
Materials and Methods
We performed a comprehensive medical record search for the years 1960 to 2006 for subjects with a diagnosis of Madelung’s deformity. Institutional review board approval was obtained for this retrospective review. Inclusion criteria were a diagnosis of Madelung’s deformity based on the classic description of distal radius and ulna abnormalities7, 8, 9, 10, 11 and adequate preoperative radiographs of the wrist, forearm, and elbow. Subjects with idiopathic and familial Madelung’s deformity were
Distal Radius Versus Entire Radius Madelung’s Deformity
We classified 31 extremities in 18 subjects as having a distal radius Madelung’s deformity (Fig. 1) and 15 extremities in 8 subjects as having an entire radius deformity (Fig. 2). The 6 subjects with unilateral Madelung’s deformity included 5 subjects with a distal radius deformity and one subject with an entire radius deformity. There were no instances of bilateral involvement in which one extremity was classified as entire radius and one as distal radius.
Radial Bow
The radial bow on the AP radiograph
Discussion
Previous descriptions of Madelung’s deformity have concentrated on the bony abnormality at the distal radius and wrist. In their classic description of the 12 features of Madelung’s deformity, Dannenberg et al7 focused on the wrist but did mention that the entire diaphysis of the radius may be involved. The deformity at the radiocapitellar joint and the increased sagittal bow of the radius were not included among the 12 features. Subsequent reports on Madelung’s deformity17, 18, 19, 20 also
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2024, Journal of Hand SurgerySimultaneous three-dimensional correction of percutaneous radial osteotomy with circular external fixator in Madelung's deformity
2022, Hand Surgery and RehabilitationMadelung-type deformity in a female individual from the Merovingian Period in Central Germany: A rare finding or a rare disease?
2021, International Journal of PaleopathologyCitation Excerpt :In modern cases, medical care results in a lower-degree deformation of the bones. Though still displaying reduced dimensions, the ulna is often not affected (cf. Zebala et al., 2007, Kouassi Koame2016). In less extreme cases, the weakness and misconduction of muscles connected to the deformation of the radius and the subluxation of the radioulnar joint, lead to reduction in dimensions.
Carpal Kinematics in Madelung Deformity
2021, Journal of Hand SurgeryCongenital Deformities of the Hands
2020, Pediatric Clinics of North AmericaCitation Excerpt :At presentation, most common chief complaints are either diffuse pain or concern about the cosmetic appearance of the distal ulna prominence, and may be bilateral. Physical examination demonstrates dorsally prominent distal ulna, dorsal concavity laterally of the distal radius, and a proportionately short forearm.26 Range of motion may be decreased in extension and ulnar deviation.
This investigation was performed at St. Louis Shriners Hospital for Children, St. Louis, MO.