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Vol. 3. Issue 1.
Pages 45-47 (January - February 2007)
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Vol. 3. Issue 1.
Pages 45-47 (January - February 2007)
DOI: 10.1016/S2173-5743(07)70208-3
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Relapsing Polychondritis Associated With a Lymphoplasmocytic Lymphoma and Eritema Nodosum
Policondritis recidivante asociada a linfoma linfoplasmocítico y eritema nudoso
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Isabel Castrejóna, Mónica Ibáñeza, Esther Vicentea, Juan Luis Steegmannb, Santos Castañedaa,??
Corresponding author
scastas@tiscali.es

Correspondence: Servicio de Reumatología. Hospital de la Princesa. Diego de León, 62. 28006 Madrid. España.
a Servicio de Reumatología, Hospital Universitario de la Princesa, Madrid, Spain
b Servicio de Hematología, Hospital Universitario de la Princesa, Madrid, Spain
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Abstract

Relapsing polychondritis is a disease of unknown etiology characterized by episodic inflammation of cartilaginous tissues. More rarely, it has been described as a paraneoplastic phenomenon mainly associated with myelodysplastic syndromes or other haematologic diseases. We present a case of relapsing polychondritis associated to low degree lymphoplasmocytic lymphoma whose picture was punctuated by cutaneous erythema nodosum and anterior uveitis. The clinical evolution was satisfactory with glucocorticoids and rituximab treatment.

Key words:
Relapsing polychondritis
Paraneoplastic syndrome
Lymphoma
Erythema nodosum
Resumen

La policondritis recidivante es una enfermedad de etiología desconocida que se caracteriza por episodios recurrentes de inflamación de los tejidos cartilaginosos. En raras ocasiones se ha descrito como un cuadro paraneoplásico, principalmente asociado a síndrome mielodisplásico y a diferentes tipos de neoplasias hematológicas. Presentamos un caso de policondritis recidivante asociada a linfoma linfoplasmocítico de bajo grado que, en su evolución, presentó afección cutánea en forma de eritema nudoso y uveítis anterior. La evolución clínica posterior fue satisfactoria, con tratamiento inmunosupresor con glucocorticoides y rituximab.

Palabras clave:
Policondritis recidivante
Síndrome paraneoplásico
Linfoma
Eritema nudoso
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Copyright © 2007. Sociedad Española de Reumatología and Colegio Mexicano de Reumatología
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